A case is reported of a 28 year old man referring the appearance of swollen blisters due to insignificant trauma since birth. Later he noticed progressive changes of the skin as teleangectasies, atrophic spots, sensivity to sun, dystrohic fingermails and webbing between fingers.The patient was hospitalized several times for an appropriate diagnosis and asked for the permission to undergo an operation of plastic surgery in Paris to correct webbing of the hands.
The rare association of two congenital diseases, epidermolysis bullosa dystrophica and poikiloderma, leads to the diagnosis of a Kindler syndrome.
LONDON, February 11 /PRNewswire/ -- Manpower Software plc, a leading provider of workforce optimisation and electronic rostering solutions, is pleased to announce that Imperial College Healthcare NHS Trust has selected Manpower Software's MAPS Healthroster solution.
David Foster, Executive Sponsor for the e-rostering project at Imperial College Healthcare NHS Trust, commented: "This is a fantastic development in what is a very progressive organisation. The system enables ward sisters to produce safe, fair and cost effective rosters and is helping us to focus on providing the right numbers of nurses with the right skills to enhance patient care. I am also excited about extending it to other work groups."
BARCELONA, Spain, February 11 /PRNewswire/ --
In the news release, Next Generation of Microsoft Innovation Focuses on Mobile Consumer, issued today, Feb. 11, by Microsoft over PR Newswire, we are advised by the company that the subhead should read, "Company agrees to acquire Danger Inc, unveils additional industry partnerships to heighten connected entertainment and information experience for mobile customers," rather than, "Company announces key industry partnerships to bring more connected entertainment and information to mobile customers."
BARCELONA, Spain, February 11 /PRNewswire/ --
MOBILE WORLD CONGRESS -- NeuStar, Inc. (NYSE: NSR) today announced that it is showcasing its Interaction Framework (iF) at Mobile World Congress 2008. iF enables mobile users to manage their identities, profiles, and social interactions within one simple-to-use, integrated, and secure framework based upon a user's network and handset.
Incontinentia pigmenti is a rare genodermatosis also called Bloch-Sulzberger syndrome or Bloch-Siemens, that shows early at birth or in the neonatal period.In its classical form,the cutaneous symptomatology develops through three steps.
1st step, with evidence of injuries, of erythematic-vescicular-blistered kind and one wave after another, linearly positioned and involving upper body and limbs;haematic hypereosinophilia is also present.
2nd step, that pops up between the second and the sixty life-week with papulo-lichenoid injuries,hyperkeratosic and warty, looking as elongatad striae in the distal limbs section ( knee, foot-and hand back ).
3rd step, when at third-sixth month of life dark pigmented spots appear at the upper body level, positioned like a vortex, a whirl or spurts.
The first descriptions of the disease are found again in the Textbook of Dermatology, published in 1874, "On disease of the skin, including exanthemata" London - New Sydenham Society, Hebra F.-Kaposi M.
The term "Xeroderma Pigmentosum" was coined from the hungarian dermatologist Moritz Kaposi wanting in such a way to indicate a characterized disease picture from pigmented and dry skin.
Hereditary disease, trasmitted with recessive autosomical modality, the XP is characterized from extreme photosensivity that causes strict and premature damages to level of the cutis and of the eyes. Its incidence is of 1:250000 in Europe and USA, while in Japan the relationship is of 1:40000.
German physician Otto Werner (1879-1936) described the clinical picture of this syndrome in 1904, in four sisters, defining the skin thin, tight, scleroderma-like, that mimics premature aging, with bilateral cataracts associated.
Also known by the term "Progeria" - 'prematurely old' Greek derivation, due to the fact that usually presents wrinkling and aging of face. Progeria occurs in two forms: Progeria of childhood, described by Jonathan Hutchinson (1886) and Hastings Gilford (1897), diagnosed in the first or second year of life and Progeria adultorum commonly indicated as Werner Syndrome.
Jonathan Hutchinson (1828-1913) described “A case of congenital absence of hair with atrophic condition of the skin and its appendages”. Lancet, London, 1: 923, 1886.
At the same time wrote “Congenital absence of hair and mammary glands with atrophic condition of the skin and its appendages in a boy whose mother had been almost wholly bald from alopecia areata from the age of six”. Transactions of the Medico-Chirurgical Society of Edinburgh, 69: 473-477, 1886.
Subsequently Hastings Gilford (1861-1941) wrote “On a condition of mixed premature and immature development”. Medico-Chirurgical Transactions, London, 80: 17-45, 1897 and coined the term Progeria from greek “Prematurely old”. In the year 1904 published “Progeria: a form of senilism”. Practitioner, London, 73: 188-217.
PARIS, February 11 /PRNewswire/ -- Following its growth and the significant successes achieved in 2007 in the different countries in which it operates, HR Access, international provider of Human Resources Management software applications and Human Resources Outsourcing services, today announced the strengthening of its commitment to pursue the momentum of its development.
In order to construct the future more effectively and capitalising on the recent achievements of the company, Eduardo Pontoriero, Chairman of HR Access and President, Devonshire Investors Global Solutions, has structured his teams globally into three divisions:
HR Access EMEA...
for growth with high potential in a promising region
In the last post I suggested that the U.S. learn from Europe in the use of high speed trains as a core component of a national transportation system. Trains are more energy efficient than cars, give off far less greenhouse emissions than airplanes, rarely get cancelled or delayed due to ‘weather’ or ‘flow control’ and depart and arrive near the central city. Given that America is much larger than any country currently utilizing high speed trains, it can only be a part of the transportation mix. What might the composite national transportation profile look like in 2015?
